October 11, 2011
Mealtimes aren't quite as enjoyable for people with phenylketonuria (PKU) as they are for the rest of us. Those with this genetic disorder have to get their protein by drinking a foul-tasting amino acid "formula." At the same time, they must avoid natural proteins - eschewing burgers, ice cream and even regular bread - because they lack the enzyme needed to process phenylalanine, one of the 19 amino acids that comprise protein.